RESUMEN

La enfermedad pulmonar intersticial (EPI) en ausencia de algún proceso infeccioso y/o neoplásico engloba varios trastornos respiratorios, los cuales tienen presentación clínica variable (aguda, subaguda o crónica). Debido a que son entidades con histologías diferentes, cursan con diferentes grados de inflamación y fibrosis que al progresar muestran rasgos cicatrizales variables donde el pulmón terminal es el resultado final de esta progresión, perdiendo sus características específicas, lo que imposibilita diferenciarlas en forma adecuada.

PALABRAS CLAVE

Fibrosis pulmonar idiopática, tomografía computada de alta resolución, neumonía intersticial usual, discusión multidisciplinaria.

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