ABSTRACT

The primary pulmonary lymphoma is very rare, while the extranodal presentation represents the 25 to 50% of the cases of non-Hodgkin’s lymphoma. The primary pulmonary commitment represents only 3 to 4% of non-Hodgkin’s lymphoma and 0.5 to 1% of the primary pulmonary neoplasms. The prevalence of pulmonary lymphoma within the lung tumors is 13% in adults. Endobronchial presentation as a manifestation of primary pulmonary lymphoma, only occurs in 0.4% of the cases. Is defined as primary pulmonary lymphoma, to the proliferation of atypical lymphoid one or both lungs in a patient with undetectable extrapulmonary disease. We report a case of anaplastic lymphoma endobronchial large cell lung primary, ALK-1 positive, which is a prognostic marker of this entity.

KEYWORDS

Anaplastic large cell lymphoma, ALK-1 positive, lung.

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