ABSTRACT

Among arteriovenous malformations, unilateral agenesis of a pulmonary artery (UPAA) is definitely considered one of the rarest, with few cases described in the literature, and its number decreasing in pediatric cases. The case of a female infant with a history of wet cough and episodes of hemoptysis is presented, which leads to performing a contrast-enhanced TACAR and diagnosing agenesis of the pulmonary artery.

KEYWORDS

Arteriovenous malformations, hemoptysis, agenesis of pulmonary artery.

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